Low Grade Fibromyxoid Sarcoma
Clinical
- Age 3-78 years, median age in 30’s
- 1-23 cm
- Predominantly trunk and lower extremities
- Rare cases in mesentery and retroperitoneum
- Most in deep soft tissue
- About 10% in some series in subcutaneous tissue
- Recurrence rate 10-75%
- May take up to 15 years to recur
- Metastatic rate 6-60%
- Higher numbers may represent cases not treated initially as sarcomas
- Rare cases reported with dedifferentiation after multiple recurrences
- Anaplasia, increased cellularity, increased mitotic rate
- Short survival after dedifferentiation
