Adult Fibrosarcoma
Clinical
- Over age 10 by definition
- Most 40-55 years
- Virtually always in deep soft tissues
- May occur superficially as dedifferentiated DFSP
- Most common in legs and trunk
- Very rare in retroperitoneum and mediastinum
- May occur in retroperitoneum as component of dedifferentiated liposarcoma
- Recurrence and distant metastatic rate about 50%
- Lymph node metastases rare
