Lipoblastoma / Lipoblastomatosis
Clinical
- Usually under age 3
- Presentation over age 20 is very rare
- Site
- May involve both trunk and extremities
- Most are circumscribed, subcutaneous
- Less commonly deep in skeletal muscle, retroperitoneum, mesentery
- Behavior
- Superficial lesions rarely recur
- Deep lesions repeatedly recur
- No metastases
- One report of associated nervous system disorders in 17% of patients (Coffin)
