Primary Amyloidosis
Classification / Lists
Plasma cell neoplasms / Immunosecretory disorders (WHO 2008)
- Monoclonal gammopathy of undetermined significance (MGUS)
- Plasma cell myeloma
- Variants:
- Non-secretory
- Smoldering
- Plasma cell leukemia
- Variants:
- Plasmacytoma
- Solitary plasmacytoma of bone
- Extraosseus (extramedullary) plasmacytoma
- Monoclonal immunoglobulin deposition diseases
- Osteosclerotic myeloma (POEMS syndrome)
- Heavy chain diseases (variants of lymphoma rather than plasma cell neoplasms)
- Gamma heavy chain disease (see lymphoplasmacytic lymphoma)
- Mu heavy chain disease (see chronic lymphocytic leukemia)
- Alpha heavy chain disease / immunoproliferative small intestinal disease (variant of extranodal marginal zone lymphoma)