Alveolar Soft Part Sarcoma
Clinical
- Age range 2-70 years, most are 15-35 years
- Location
- 60% extremities (frequently thigh)
- 20% trunk
- 12% head and neck
- 8% retroperitoneum
- Unusual sites include oral cavity, uterus
- Over half present with metastases
- Frequent metastatic sites lung and brain
- Primary may be occult
- Metastasis and death may occur late (>10 years), even if clearly excised with no local recurrence
- 5 year survival 60% but 20 year survival 15%
- Pediatric cases may have better survival
