Aggressive Angiomyxoma

Clinical

Nearly all age 20-50 years
- Reports of 13, 8 and 1 year old males
- One report in an 11 year old female
Most occur in females
- About 5% in males
Virtually restricted to soft tissue of perineum, external genitalia, inguinal region in both sexes
- Rarely in vagina or pelvis in females
Usually over 10 cm
- Rarely under 5 cm
Can recur
- Current recurrence rate is significantly lower than reported in early series
- Two cases of metastasis reported, one with death