Extra-abdominal Desmoid Fibromatosis
Supplemental Studies
Immunohistology
| Beta-catenin | positive |
| Actin | positive |
| Desmin | usually negative, occasionally focal |
| CD34 | negative |
| S100 | negative |
| Keratin | negative |
| Estrogen receptor | 0-10% |
| Progesterone receptor | 0-25% |
| Cathepsin-D | positive |
Genetics
Trisomies 8 and 20, common in extra-abdominal desmoids are rare in abdominal desmoids

