DFSP may dedifferentiate with a fibrosarcoma pattern
If fibrosarcoma occurs in the dermis or subcutaneous tissue, it is usually dedifferentiated DFSP
Wide age range but most common 20-40 years of age
Trunk most common, followed by proximal extremities and head and neck
Very rare cases of similar appearing tumors in deep tissues and retroperitoneum
Same clinical behavior
Early lesions are plaque-like
Late lesions protuberant
10-20% recur if widely excised
Frequent, aggressive recurrences if not widely excised
Metastases <5% if widely excised
Cases with areas of sarcoma appear to have the same behavior as usual cases if widely excised
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