Lipofibromatosis
Supplemental Studies
Immunohistology
Spindled fibroblastic cells| CD99 | 10/12 |
| CD34 | 12/13 |
| Smooth muscle actin | 10/12 |
| bcl2 | 7/12 |
| S100 | 5/14 |
| Muscle specific actin | 3/13 |
| EMA | 2/12 |
| Desmin | neg |
| Keratin | neg |
| Beta-catenin | neg |
Pigmented spindle cells (rare)
| Tyrosinase | 2/2 |
| MelanA | 2/2 |
| HMB45 | 1/2 |
| S100 | 1/2 |

