Appendiceal Mucinous Neoplasm with High Risk of Recurrence
Clinical
- Frequent cause of pseudomyxoma peritonei
- Abundant mucin secretion by implants
- Causes abdominal distention
- Long clinical course
- Multiple recurrences
- Surgical debulking is worthwhile, both at presentation and for recurrences
- 50% 5 year, 20% 10 year survival
- Death usually caused by intestinal obstruction after multiple recurrences
- Some question as to whether or not right colectomy is indicated
- Frequent involvement of ovary
- In all cases of appendiceal mucinous neoplasms, the ovaries should be examined
- In all cases of ovarian mucinous neoplasms, the appendix should be examined (or removed)
- In all cases of pseudomyxoma peritonei the appendix and the ovaries should be examined
